An "Anaplastic" Kaposi's Sarcoma Mimicking a Stewart-Treves Syndrome. A Case Report and a Review of Literature
Identifieur interne : 000448 ( France/Analysis ); précédent : 000447; suivant : 000449An "Anaplastic" Kaposi's Sarcoma Mimicking a Stewart-Treves Syndrome. A Case Report and a Review of Literature
Auteurs : Dimitri Salameire [France] ; Isabelle Templier [France] ; Julie Charles [France] ; Nicole Pinel [France] ; Patrice Morand [France] ; Marie-Therese Leccia [France] ; Sylvie Lantuejoul [France]Source :
- The American journal of dermatopathology [ 0193-1091 ] ; 2008.
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- Pascal (Inist)
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- topic : Homme.
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- KwdEn :
Abstract
Cutaneous angiosarcoma (AGS) developing in a lymphedematous arm, after lymphadenectomy in the context of breast cancer, is the definition of the classical Stewart-Treves syndrome. Like AGS, many tumors such as Kaposi's sarcoma (KS) could develop in chronic lymphedema. We describe the case of a 50-year-old woman who presented with several nodules on the left lymphedematous arm evocative of a Stewart-Treves syndrome, 2 years after a left mastectomy and a homolateral lymphadenectomy. The histological examination revealed an atypical vascular proliferation suggesting AGS, but endothelial atypical cells nuclei were strongly stained by herpes human virus 8 antibody. The final diagnosis was an "anaplastic" KS mimicking a Stewart-Treves syndrome. The total regression of the lesion was obtained by elastic contention and intradermic liposomal doxorubicin. "Anaplastic" KS is a rare histological form of nodular KS, which mimics a cutaneous AGS but classically expresses herpes human virus 8. It is essential to know about this entity, particularly in a lymphedematous arm, to avoid aggressive treatment such as amputation.
Affiliations:
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Pascal:08-0275943Le document en format XML
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<term>Chronic</term>
<term>Dermatology</term>
<term>Differential diagnostic</term>
<term>Herpes</term>
<term>Human</term>
<term>Human herpesvirus 8</term>
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<term>Peau</term>
<term>Herpès</term>
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<term>Virus</term>
<term>Herpesvirus hominis 8</term>
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<front><div type="abstract" xml:lang="en">Cutaneous angiosarcoma (AGS) developing in a lymphedematous arm, after lymphadenectomy in the context of breast cancer, is the definition of the classical Stewart-Treves syndrome. Like AGS, many tumors such as Kaposi's sarcoma (KS) could develop in chronic lymphedema. We describe the case of a 50-year-old woman who presented with several nodules on the left lymphedematous arm evocative of a Stewart-Treves syndrome, 2 years after a left mastectomy and a homolateral lymphadenectomy. The histological examination revealed an atypical vascular proliferation suggesting AGS, but endothelial atypical cells nuclei were strongly stained by herpes human virus 8 antibody. The final diagnosis was an "anaplastic" KS mimicking a Stewart-Treves syndrome. The total regression of the lesion was obtained by elastic contention and intradermic liposomal doxorubicin. "Anaplastic" KS is a rare histological form of nodular KS, which mimics a cutaneous AGS but classically expresses herpes human virus 8. It is essential to know about this entity, particularly in a lymphedematous arm, to avoid aggressive treatment such as amputation.</div>
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